A 6-month-old infant has been exclusively fed a commercially available infant formula. Upon introduction of fruit juices, however, the child develops jaundice, hepatomegaly, vomiting, lethargy, irritability, and seizures. Tests for urine-reducing substances are positive. Which of the following is likely to explain this child’s condition?

a. Tyrosinosis

b. Galactosemia

c. Fructosemia

d. a1-antitrypsin

e. Glucose-6-phosphatase deficiency

the answer is below…

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